Progressive facial and cerebral hemiatrophy: Parry-Romberg syndrome or scleroderma "en coup de sabre"?
نویسنده
چکیده
Acta Neurologica Taiwanica Vol 13 No 4 December 2004 From the Department of Neurology, Chang Gung Memorial Hospital, Linkou Medical Center, Taoyuan, Taiwan. Received November 19, 2004. Revised and Accepted November 29, 2004. Reprint requests and correspondence to: Nai-Shin Chu, MD. Department of Neurology, Chang Gung Memorial Hospital, No. 199, Tung-Hwa N. Road, Taipei, Taiwan. E-mail: [email protected] Progressive Facial and Cerebral Hemiatrophy: Parry-Romberg Syndrome or Scleroderma “en Coup de Sabre” ?
منابع مشابه
Parry-Romberg Syndrome Associated with Localized Scleroderma
Parry-Romberg syndrome is a rare neurocutaneous disorder of unknown origin. It is characterized by progressive facial hemiatrophy and frequently overlaps with a condition known as linear scleroderma 'en coup de sabre'. Neurological involvement is frequently described in these patients, including migraine, facial pain and epilepsy, which represent the commonest neurological conditions, sometimes...
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Parry Romberg syndrome(PRS) is a rare acquired poorly understood neurocutaneous syndrome of unknown etiology characterized by slow progressive atrophic changes commonly affecting one half of the face. The exact incidence and etiology towards the syndrome remains unclear. Apart from the multifactorial etiology proposed, the possible primary cause is mainly attributed to the cerebral disturbance ...
متن کاملLate-onset progressive facial hemiatrophy (Parry-Romberg syndrome).
Initially described by Parry in 1825 and systematized by Romberg in 1846, progressive facial hemiatrophy syndrome is a controversial and poorly understood entity, with sporadic occurrence and no known mendelian inheritance. It is a slowly progressive disorder, affecting chiefly females in their first and second decades of life, characterized by unilateral atrophy of facial tissues, mostly skin ...
متن کاملParry-Romberg Syndrome with En Coup de Sabre
Parry-Romberg syndrome (PRS) is a relatively rare degenerative disorder that is poorly understood. PRS is characterized by slowly progressing atrophy affecting one side of the face, and is frequently associated with localized scleroderma, especially linear scleroderma, which is known as en coup de sabre. This is a report of the author's experiences with PRS accompanying en coup de sabre, and a ...
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BACKGROUND Linear scleroderma "en coup de sabre" (LSCS) usually affects one side of the face and head in the frontoparietal area with band-like indurated skin lesions. The disease may be associated with facial hemiatrophy. Various ophthalmological and neurological abnormalities have been observed in patients with LSCS. We describe an unusual case of LSC. CASE PRESENTATION A 23 year old woman ...
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ورودعنوان ژورنال:
- Acta neurologica Taiwanica
دوره 13 4 شماره
صفحات -
تاریخ انتشار 2004